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Hereditary Pancreatitis

Hereditary pancreatitis is an autosomal dominant disorder that presents as a dysfunction of the pan-

Fig. 4.20. Hereditary pancreatitis. CT image of shrunken pancreas with calcifications. The patient's father had a similar CT appearance

creas (inflammation) during the first decade of life. Usually each episode will last between 2 days and 2 weeks. US will reveal a shrunken fibrotic pancreas with calcifications, and CT will show dilatation of the ductal system, pancreatic stones or pancreatic complications (Fig. 4.20). Approximately 15% of patients with hereditary pancreatitis may have pancreatic carcinoma in adulthood.

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